[Thrombotic microangiopathies]

O.J. Nielsen; L. Friis-Hansen

[Thrombotic microangiopathies]

Abstract

The thrombotic microangiopathic diseases, which include acquired and congenital TTP and HUS, are most frequently acute disease entities. Untreated, these diseases are associated with a lethal course in many cases. Deficiency of the von Willebrand cleaving enzyme, ADAMTS13, is a decisive pathophysiological defect in most cases of thrombotic microangiopathic diseases. Early recognition and a secure distinction from other conditions that resemble TMA diseases is essential in order to institute adequate treatment and to obtain a favourable outcome in terms of both survival and development of serious sequelae
Udgivelsesdato: 2009/11/30

Originalsprog	Dansk
Tidsskrift	Ugeskrift for læger
Vol/bind	171
Udgave nummer	49
Sider (fra-til)	3614-3620
Antal sider	6
ISSN	0041-5782
Status	Udgivet - 2009

Citationsformater

@article{1b553310626d11df928f000ea68e967b,

title = "[Thrombotic microangiopathies]",

abstract = "The thrombotic microangiopathic diseases, which include acquired and congenital TTP and HUS, are most frequently acute disease entities. Untreated, these diseases are associated with a lethal course in many cases. Deficiency of the von Willebrand cleaving enzyme, ADAMTS13, is a decisive pathophysiological defect in most cases of thrombotic microangiopathic diseases. Early recognition and a secure distinction from other conditions that resemble TMA diseases is essential in order to institute adequate treatment and to obtain a favourable outcome in terms of both survival and development of serious sequelae Udgivelsesdato: 2009/11/30",

author = "O.J. Nielsen and L. Friis-Hansen",

note = "Cochrane: Den danske tekst klippet hertil, De trombotiske mikroangiopatier, og den engelske tekst downloadet.",

year = "2009",

language = "Dansk",

volume = "171",

pages = "3614--3620",

journal = "Ugeskrift for l{\ae}ger",

issn = "0041-5782",

publisher = "Almindelige Danske Laegeforening",

number = "49",

}

TY - JOUR

T1 - [Thrombotic microangiopathies]

AU - Nielsen, O.J.

AU - Friis-Hansen, L.

N1 - Cochrane: Den danske tekst klippet hertil, De trombotiske mikroangiopatier, og den engelske tekst downloadet.

PY - 2009

Y1 - 2009

N2 - The thrombotic microangiopathic diseases, which include acquired and congenital TTP and HUS, are most frequently acute disease entities. Untreated, these diseases are associated with a lethal course in many cases. Deficiency of the von Willebrand cleaving enzyme, ADAMTS13, is a decisive pathophysiological defect in most cases of thrombotic microangiopathic diseases. Early recognition and a secure distinction from other conditions that resemble TMA diseases is essential in order to institute adequate treatment and to obtain a favourable outcome in terms of both survival and development of serious sequelae Udgivelsesdato: 2009/11/30

AB - The thrombotic microangiopathic diseases, which include acquired and congenital TTP and HUS, are most frequently acute disease entities. Untreated, these diseases are associated with a lethal course in many cases. Deficiency of the von Willebrand cleaving enzyme, ADAMTS13, is a decisive pathophysiological defect in most cases of thrombotic microangiopathic diseases. Early recognition and a secure distinction from other conditions that resemble TMA diseases is essential in order to institute adequate treatment and to obtain a favourable outcome in terms of both survival and development of serious sequelae Udgivelsesdato: 2009/11/30

M3 - Tidsskriftartikel

SN - 0041-5782

VL - 171

SP - 3614

EP - 3620

JO - Ugeskrift for læger

JF - Ugeskrift for læger

IS - 49

ER -