Idebenone increases mitochondrial complex I activity in fibroblasts from LHON patients while producing contradictory effects on respiration

Claire Angebault, Naig Gueguen, Valerie Desquiret-Dumas, Arnaud Chevrollier, Virgine Guillet, Christophe Verny, Julien Cassereau, Marc Ferre, Dan Milea, Patrizia Amati-Bonneau, Dominique Bonneau, Vincent Procaccio, Pascal Reynier, Dominique Loiseau