Abstract
OBJECTIVE: To explore specific clinical issues, surgical results, and complications of 80 cochlear implantations (CI) in 55 patients with Pendred syndrome (PS) or non-syndromic enlarged vestibular aqueduct (NSEVA).
BACKGROUND: Previous studies have focused either on unselected case series or on populations with mixed cochlear malformations. PS/NSEVA accounts for up to 10% of congenital SNHL, rendering this a large group of cochlear implant candidates. The abnormal inner ear anatomy of these patients may be associated with a lower surgical success rate and a higher rate of complications.
STUDY DESIGN: Retrospective review of patients' medical records and CT/MRI.
SETTING: Tertiary referral center.
MATERIALS AND METHODS: The medical records and CT/MRI images of 55 PS/NSEVA patients receiving 80 cochlear implantations from 1982-2014 were reviewed. Demographic data, surgical results, intra-operative incidents, and post-operative complications were retrieved.
RESULTS: Complications occurred in 36% of implantations; 5% hereof major complications. Gushing/oozing from the cochleostoma occurred in 10% of implantations and was related to transient, but not prolonged post-operative vertigo.
CONCLUSION: Intra-operative risks of gushing/oozing and post-operative vertigo are the primary clinical issues in PS/NSEVA patients regarding CI. Nonetheless, the surgical success rate is high and the major complication rate is low; similar to studies of unselected series of CI recipients.
| Original language | English |
|---|---|
| Journal | Acta Oto-Laryngologica |
| Volume | 136 |
| Issue number | 10 |
| Pages (from-to) | 1064-8 |
| Number of pages | 5 |
| ISSN | 0001-6489 |
| DOIs | |
| Publication status | Published - 2 Oct 2016 |
Keywords
- Child
- Child, Preschool
- Cochlear Implantation
- Denmark
- Female
- Goiter, Nodular
- Hearing Loss, Sensorineural
- Humans
- Infant
- Infant, Newborn
- Male
- Postoperative Complications
- Retrospective Studies
- Vestibular Aqueduct
- Journal Article