[Catecholaminergic polymorphic ventricular tachycardia is a rare inherited heart disease.]

Anders Gaarsdal Holst, 1jacob Tfelt-Hansen, Morten S Olesen, Juliane Theilade, Bo G Winkel, Alex H Christensen, Henning Bundgaard, Stig Haunsø, Jesper Hastrup Svendsen

Abstract

Catecholaminergic polymorphic ventricular tachycardia is a rare inherited heart disease, which can lead to life-threatening ventricular arrhythmias in patients with a structurally normal heart. The age of onset is usually between two and 12 years and the initial symptom is frequently syncope or cardiac arrest. The arrhythmias are usually triggered by exercise or emotional affection. The diagnosis is often made using exercise electrocardiogram, which typically triggers arrhythmias. The treatment consists of beta blockers, frequently in combination with implantation of a cardioverter-defibrillator.

Original languageDanish
JournalUgeskrift for læger
Volume172
Issue number31
Pages (from-to)2140-2144
Number of pages4
ISSN0041-5782
Publication statusPublished - Aug 2010

Cite this