Massive Electrical Storm at Disease Onset in a Patient with Brugada Syndrome

TY - JOUR

T1 - Massive Electrical Storm at Disease Onset in a Patient with Brugada Syndrome

AU - Pallisgaard, Jannik L

AU - Gang, Uffe

AU - Kanters, Jørgen K.

AU - Hansen, Peter R

PY - 2014/12/16

Y1 - 2014/12/16

N2 - Objective:Background: Brugada syndrome (BrS) is a genetic arrhythmogenic disease characterized by ST-segment elevations in the right precordial leads of the electrocardiogram (ECG). These ECG changes may be concealed and BrS may present with electrical storm characterized by recurrent ventricular tachycardia and fbrillation.Case Report: A 49-year-old previously healthy man was admitted with electrical storm. The patient received direct current (DC) cardioversion shocks and only after intravenous lidocaine did the electrical storm slowly subside with a total of 255 DC shocks administered during the frst 24 h after admission. He fully recovered and received an implantable cardioverter-defbrillator. Subsequent drug challenge with fecainide revealed type 1 BrS.Conclusions: Massive electrical storm can be the frst symptom of BrS and the diagnostic ECG changes may be concealed at presentation. Although hundreds of DC shocks may be required during initial treatment, full recovery can be achieved.

AB - Objective:Background: Brugada syndrome (BrS) is a genetic arrhythmogenic disease characterized by ST-segment elevations in the right precordial leads of the electrocardiogram (ECG). These ECG changes may be concealed and BrS may present with electrical storm characterized by recurrent ventricular tachycardia and fbrillation.Case Report: A 49-year-old previously healthy man was admitted with electrical storm. The patient received direct current (DC) cardioversion shocks and only after intravenous lidocaine did the electrical storm slowly subside with a total of 255 DC shocks administered during the frst 24 h after admission. He fully recovered and received an implantable cardioverter-defbrillator. Subsequent drug challenge with fecainide revealed type 1 BrS.Conclusions: Massive electrical storm can be the frst symptom of BrS and the diagnostic ECG changes may be concealed at presentation. Although hundreds of DC shocks may be required during initial treatment, full recovery can be achieved.

U2 - 10.12659/AJCR.892314

DO - 10.12659/AJCR.892314

M3 - Journal article

C2 - 25528772

SN - 0022-0736

VL - 15

SP - 559

EP - 561

JO - Journal of Electrocardiology

JF - Journal of Electrocardiology

ER -